• Disulfide cross-linked multimers of TDP-43 and spinal motoneuron loss in a TDP-43A315T ALS/FTD mouse model 

      Bargsted L., Medinas D.B., Martínez Traub F., Rozas P., Muñoz N., Jerez C., Court F.A., Hetz C., Matus S.; Nassif, Melissa [Centro de Biología Integrativa, Facultad de Ciencias, Universidad Mayor, Chile]; Catenaccio, Alejandra [Centro de Biología Integrativa, Facultad de Ciencias, Universidad Mayor, Chile] (Nature Publishing Group, 2017)
      Tar DNA binding protein 43 (TDP-43) is the principal component of ubiquitinated protein inclusions present in nervous tissue of most cases of both amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD). ...


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