Listar INVESTIGACIÓN por autor "de la Barca, Juan Manuel Chao"
Mostrando ítems 1-1 de 1
-
The Metabolomic Signature of Opa1 Deficiency in Rat Primary Cortical Neurons Shows Aspartate/Glutamate Depletion and Phospholipids Remodeling
Arrazola, Macarena S. [Univ Mayor, Fac Ciencias, Ctr Integrat Biol, Santiago, Chile]; de la Barca, Juan Manuel Chao; Bocca, Cinzia; Arnaune-Pelloquin, Laetitia; Iuliano, Olga; Tcherkers, Guillaume; Lenaers, Guy; Simard, Gilles; Belenguer, Pascale; Reynier, Pascal (NATURE PUBLISHING GROUP, 2019)Pathogenic variants of OPA1, which encodes a dynamin GTPase involved in mitochondrial fusion, are responsible for a spectrum of neurological disorders sharing optic nerve atrophy and visual impairment. To gain insight on ...